Abstract

Retinitis pigmentosa (RP) is a group of genetic retinal dystrophies characterized by nightblindness, visual field depression, intraretinal bone-spicule-like pigmentation, narrowing of the retinal vessels, and a reduction in the amplitude of the electroretinogram. Usher's syndrome is a variant of RP in which there is also a congenital neurosensory hearing defect. Although the loss of visual function in RP typically is more severe in the retinal periphery, there is ultimately a reduction in foveal function in a substantial number of RP patients.

© 1985 Optical Society of America